| 11. | Analyses have revealed a mixture of biopolymers, containing mainly long chain fatty acids, phenylpropanoids, phenolics and traces of carotenoids.
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| 12. | A non-functional D-BP protein results in the abnormal accumulation of long chain fatty acids and bile acid intermediates.
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| 13. | Beta-oxidation of long chain fatty acids produces two carbon units, acetyl-CoA and the reducing equivalents NADH and FADH2.
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| 14. | The very long chain fatty acid ( > 18 carbon atoms ) content ranged from 0.44 to 1.37 %.
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| 15. | This results in the over-accumulation of very long chain fatty acids and branched chain fatty acids, such as phytanic acid.
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| 16. | It is an elongase that appears to be involved in the production of very long chain fatty acids that are 26 carbons and longer.
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| 17. | In X-ALD patients, abnormally high levels of very long chain fatty acid ( VLCFA ) accumulate in various body tissues and fluids.
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| 18. | Bulkier long chain fatty acids are bound by a fatty acid-binding tunnel that is located in the N-terminal domain of each monomer.
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| 19. | It is classified in the sub-group of very long chain fatty acids ( VLCFA ), which includes molecules containing more than 20 carbon atoms.
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| 20. | Biochemically, individuals with ALD show very high levels of unbranched, saturated, very long chain fatty acids, particularly cerotic acid ( 26 : 0 ).
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